Rapidly progressive, pauci-immune diffuse crescentic glomerulonephritis in an infant
作者： Hiroshi Tanaka , Shinobu Waga , Koichi Suzuki , Tohru Nakahata , Hiroshi Kawachi
DOI: 10.1007/S00467-002-0938-7
关键词:
摘要: A Japanese male infant presented with nephrotic syndrome at 41 days. His renal function progressively deteriorated, and he died 4 months of the age. An open biopsy revealed diffuse crescentic glomerulonephritis (CrGN) without immune complex deposition, which is not characteristic congenital (CNS). Examination for nephrin antigen using rabbit anti-nephrin extra- intracellular site antibodies was positive. These clinical observations suggest that patient had a unique histological variant CNS. This first report rapidly progressive, pauci-immune CrGN in infancy.
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