Impact of the Revision of Arrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia Task Force Criteria on Its Prevalence by CMR Criteria

摘要: Objectives The purpose of our study was to assess the impact revised versus original criteria on prevalence arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) in cardiac magnetic resonance (CMR) studies. Background Recently, ARVC/D task force have been revised, aiming for a better diagnostic sensitivity. implications this revision clinical decision making are unknown. Methods We retrospectively evaluated CMR scans 294 patients referred between 2005 and 2010, determined presence or absence major minor using criteria. Previously, abnormalities were identified by ventricle dilation (global segmental), microaneurysm, regional hypokinesis. require combination severe wall motion (akinesis dyskinesis dyssynchrony) with global dysfunction (quantitative assessment). Results Applying criteria, 69 (23.5%) had 19 (6.5%) Forty-three (62.3%) did not meet any Using 172 (58.5%) at least 1 criterion 12 (4%) criteria; 167 (97%) In subgroup 134 complete work-up ARVC, 10 met diagnosis proven without counting imaging Only 4 according none However, 112 124 correctly classified as negative (specificity 94% 96%, respectively). Conclusions experience, significantly reduced overall revision, although maintaining high specificity, may improved sensitivity identifying ARVC/D. Larger studies including follow-up required.