Epileptic encephalopathy with continuous spike-waves during sleep: the need for transition from childhood to adulthood medical care appears to be related to etiology.
作者： Anne de Saint-Martin , Gabrielle Rudolf , Caroline Seegmuller , Maria Paola Valenti-Hirsch , Edouard Hirsch
DOI: 10.1111/EPI.12724
关键词:
摘要: Epileptic encephalopathy with continuous diffuse spike-waves during slow-wave sleep (ECSWS) presents clinically infrequent nocturnal focal seizures, atypical absences related to secondary bilateral synchrony, negative myoclonia, and atonic rare generalized tonic-clonic seizures. The unique electroencephalography (EEG) pattern found in ECSWS consists of continuous, diffuse, sleep. Despite the eventual disappearance clinical seizures EEG abnormalities by adolescence, prognosis is guarded most cases because neuropsychological behavioral deficits. has a heterogeneous etiology (genetic, structural, unknown). Because epilepsy epileptic are self-limited age related, need for ongoing medical care transition adult might be questioned. For adolescents whom remains unknown (possibly genetic) who experience abnormalities, there rarely long-term neurologic follow-up, often relatively normal cognitive social evolution follows. However, majority patients structural possibly "genetic syndromic" etiologies will have persistent deficits suitable socioeducative care. Therefore, process depend mainly on its features (epileptic active phase duration, evolution) revolve around support rather than pharmacologic follow-up.
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