Mitochondrial respiratory chain supercomplexes are destabilized in Barth Syndrome patients.
作者： Matthew McKenzie , Michael Lazarou , David R. Thorburn , Michael T. Ryan
DOI: 10.1016/J.JMB.2006.06.057
关键词:
摘要: … Here, we examine the steady-state levels of the respiratory chain complexes and the supercomplexes in cells from Barth Syndrome patients. The cardiolipin defects present in Barth …
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