Arrhythmogenic right ventricular dysplasia/cardiomyopathy: need for an international registry. European Society of Cardiology and the Scientific Council on Cardiomyopathies of the World Heart Federation.

摘要: Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy. right ventricular dysplasia/cardiomyopathy (ARVD/C) is a heart muscle disease characterized by peculiar involvement and electrical instability that precipitates arrhythmias sudden death. The purpose of the present consensus report Study Group European Society Cardiology Scientific Council on Cardiomyopathies World Heart Federation to review considerable progress in our understanding etiopathogenesis, morbid anatomy, clinical presentation ARVD/C since its first description 1977. This article will focus important hut still unanswered issues, mostly regarding risk stratification, outcome, management affected patients. Because relatively uncommon any one center may have experience with only few patients, an international registry being established accumulate information enhance numbers patients can be analyzed answer pending questions. also facilitate pathologic, molecular, genetics research etiology pathogenesis disease. Furthermore, availability database awareness this largely unrecognized condition among medical community. Physicians are encouraged enroll International Registry ARVD/C.