Gastrointestinal autonomic nerve tumor presenting as high-grade sarcoma. Case report and review of the literature.

摘要: Gastrointestinal autonomic nerve (GAN) tumors, also known as plexosarcomas, are a rare distinct subtype of the gastrointestinal stromal tumors. These tumors usually histologically low-grade, epithelioid or spindle-cell neoplasms that can be distinguished from other on basis their unique ultrastructural features. A 66-year-old female presented with high-grade sarcoma small bowel. Ultrastructural studies showed features GAN tumor. The light microscopic and described. tumor cells gave strong, diffuse staining for vimentin synaptophysin, weak focal neuron-specific enolase S100. While presenting low-grade histologic examination, this case demonstrates should considered in differential diagnosis tract, especially when evidence smooth muscle, peripheral sheath, neuroblastic origin is not forthcoming.