作者: Albert Aynsley-Green , Charles A Stanley , Khalid Hussain
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摘要: Congenital hyperinsulinism of infancy is the commonest cause persistent and recurrent hypoglycaemia in neonatal period. It a heterogeneous disorder with respect to clinical presentation, histology, molecular biology genetics. The biochemical profile one hypoketotic, hypofattyacidemic hypoglycemia. To prevent permanent brain damage from hypoglycemia, treatment infants congenital must be prompt aggressive. drugs used medical therapy for are diazoxide, octreotide, glucagon nifedipine.