Liver transplantation for hereditary tyrosinemia type I: analysis of the UNOS database.
作者： Ronen Arnon , Rachel Annunziato , Tamir Miloh , Melissa Wasserstein , Hiroshi Sogawa
DOI: 10.1111/J.1399-3046.2011.01497.X
关键词:
摘要: Patients with HT-1 can develop progressive liver disease and have a high incidence of HCC. LT is indicated in patients fulminant failure, HCC or decompensated chronic refractory to NTBC. To determine the need for outcomes after children HT-1. Children who had between 10/1987 5/2008 were identified from UNOS database. Of 11,467 database, 125 (1.1%) required secondary Mean age at was two half yr (s.d. ± 3.6 yr). during first 10 study (1.82, s.d. 2.86 yr) significantly lower than last decade (3.70, 4.42 yr), p = 0.01. Nearly (58, 46.4%) transplanted 1988 1992. Overall, one- five-yr patient survival 90.4% 90.4%, respectively. valuable option failure when medical treatment fails. The rate has decreased transplant increased over most probably reflecting effect early diagnosis
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