作者: F. A. Wijburg , W. Ch. C. Reitsma , M. J. H. Slooff , F. J. van Spronsen , H. A. Koetse
DOI: 10.1007/BF00711743
关键词:
摘要: Dietary treatment cannot prevent a lethal outcome in many patients with hereditary tyrosinaemia type I (van Spronsen et al 1994). Therefore, until the discovery of 2-(2-nitro-4-trifluoromethylbenzoyl)-1,3-cyclohexanedione (NTBC) as potential drug (Lindstedt 1992), orthotopic liver transplantation (OLT) was only definitive this disease 1989). We report our experiences OLT 9 I.